Best Disease in 13 Years Old Female

Clinical Image

Austin Ophthalmol. 2021; 5(1): 1020.

Best Disease in 13 Years Old Female

Naya K*, Lidya I, Hasnaoui I, Tazi H, Erradi A, Bardi C, Abdallah E and Berraho A

Department of Ophthalmology B, Ibn-Sina University Hospital, Rabat, Morocco

*Corresponding author: Kaoutar Naya, Department of Ophthalmology B, Ibn-Sina University Hospital, Rabat, Morocco

Received: May 25, 2021; Accepted: June 05, 2021; Published: June 12, 2021

Clinical Image

Best disease is a hereditary-degenerative macular dystrophy. Described for the first time by Friedrich Best, It is due to the accumulation of lipofuscin in the macular pigment epithelium. We report a case of a 13 years old female with no medical history. Slit lamp examination revealed unremarkable findings in the anterior segment of both eyes. Posterior segment exam, at the macula, showed a well circumscribed yellow material similar to the egg yolk structure, in both eyes (Figure 1).

Figure 1: Retinography with bilateral egg yolk-like image on macula.

    

    
    

    

    Figure 1: Retinography with bilateral egg yolk-like image on macula.

The Optical Coherence Tomography (OCT) macula revealed Pigmentary Epithelial Detachment (PED) and LE atrophic scar. The systemic examination had no remarkable findings. The patient was diagnosed Best Vitelliform macula.

Citation:Naya K, Lidya I, Hasnaoui I, Tazi H, Erradi A, Bardi C, et al. Best Disease in 13 Years Old Female. Austin Ophthalmol. 2021; 5(1): 1020.