Giant Cell Tumor of the Sphenoid with Clivus Extension in a Pediatric Patient

Case Report

Austin Neurosurg Open Access. 2023; 9(1): 1074.

Giant Cell Tumor of the Sphenoid with Clivus Extension in a Pediatric Patient

Garrido Ruiz PA¹*; Román Garrido M²

1Department of Neurosurgery, Hospital Universitario de Salamanca, Salamanca, Spain

2Department of Primary Care, Hospital Universitario de Salamanca, Salamanca, Spain

*Corresponding author: Patricia Alejandra Garrido Department of Neurosurgery, Hospital Universitario de Salamanca, Neurosurgery Service, 4th Floor Block D, P.o de San Vicente, 182, 37007 Salamanca, Spain. Tel: 616792305 Email: [email protected]; [email protected]

Received: March 14, 2023 Accepted: April 21, 2023Published: April 28, 2023

Abstract

We present a case of giant cell tumor of the clivus in a pediatric patient. The case is very interesting because this benign tumor is generally located in the epiphysis of long bones, and only 1% is found in the cranial vault and the base of skull. The sphenoid bone and the petrous portion of the temporal bone are the most commonly affected cranial locations, probably due to their endochondral ossification.

Keywords: Giant cell tumor; Clivus; Pediatric; Endoscopic

Case Presentation

The patient is a 13-year-old girl with a personal history of migraine and tinnitus, with a normal MRI conducted the year before. She presented oppressive temporal-parietal headache and complete ophthalmoplegia of the left eye, with ipsilateral blindness and no light perception. A CT scan reveals an expansile soft tissue mass centered in the clivus that expands anteriorly to the sphenoid bone and the posterior ethmoidal cells, with associated remodeling and patchy lytic areas in adjacent bone structures. A brain MRI shows a 4.4x2.4x2.3cm mass that suggests fibrous dysplasia or plasmacytoma.