Clinical Image
J Ophthalmol & Vis Sci. 2024; 9(2): 1095
Persistent Hyperplastic Primary Vitreous
Marrakchi Salma*; El Aouadi Salma; Allali Nazik; Chat Latifa; El Haddad Sihame
Department of Pediatric Radiology, Ibn Sina University Hospital, Rabat, Morocco
*Corresponding author: Marrakchi Salma, Department of Pediatric Radiology, Ibn Sina University Hospital, Mohamed Ben Abdellahregragui, Al Irfane, Rabat, Morocco. Tel: +212650095952 Email: marrakchi.salma@gmail.com
Received: September 16, 2024 Accepted: September 27, 2024 Published: October 04, 2024
Clinical Image
Persistent Hyperplastic Primary Vitreous (PHPV) is a congenital developmental anomaly caused by the incomplete regression of primary vitreous with the abnormal persistence of hyaloid vasculature [1]. Clinically PHPV presents with leucocoria, microphthalmia, and cataract [2]. Diagnosis can be made on imaging. Ultrasound reveals a hyperechoic structure in the vitreous chamber extending from the posterior wall of the lens to the optic disc and vascularized on color Doppler [3]. CT scan can better demonstrate all the findings of ultrasonography and aid in better visualization of the underlying pathologies [4]. On magnetic resonance imaging, PHPV appears as a triangular retrolental vascular soft tissue mass with a central stalk of hyaloid remnant connected to the optic disc [5]. The image below depicts a 3-year-old patient who presents with leucocoria. Axial CISS-T2-weighted 1.5T MR image revealed bilateral abnormal structure extending from the retrolental area to the region of the optic disc, appearing as low T2 signal against the normal T2 signal of the globe.
Figure 1:
References
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