Steatocystoma Multiplex of Scrotum

Case Report

Austin J Urol. 2015; 2(4): 1033.

Steatocystoma Multiplex of Scrotum

Kumar R, Krishnamoorthy S* and Rajamanickam MG

Department of Urology and Renal Transplantation, University of Sri Ramachandra Medical Centre, Chennai, India

*Corresponding author: Sriram Krishnamoorthy, Department of Urology and Renal Transplantation, University of Sri Ramachandra Medical Center, Chennai, India

Received: July 28, 2015; Accepted: November 12, 2015; Published: November 27, 2015

Abstract

Steatocystoma Multiplex (SM) is a hamartomatous malformation of the pilosebaceous duct. It is a rare disorder of the pilosebaceous unit, characterized by the development of numerous sebum-containing dermal cysts [1]. Here, we report a 22-year-old male presented with multiple asymptomatic, yellow to skin-colored firm cystic swellings over the scrotum; the lesion had been present for about 3 years. Histological findings are consistent with the diagnosis of steatocystoma multiplex. This case represents an unusual clinical manifestation of steatocystoma multiplex in scrotum and is presented for its rarity.

Keywords: Steatocystoma multiplex; Scrotum; Sebaceous cyst

Introduction

First described by Jamieson in 1873, and coined by Pringle in 1899, Steatocystoma Multiplex (SM) is an uncommon disorder of the pilosebaceous unit characterized by the development of numerous sebum-containing dermal cysts [1]. Historically, this condition may be hereditary (as an autosomal dominant trait) or more commonly sporadic. It usually begins in adolescence or during early adult life [1,2]. Clinically, it is characterized by multiple, small, soft, movable, yellowish-to-skin-colored dermal cystic papules and nodule and the overlying epidermis is usually normal with no central punctum.

In typical cases of SM, cysts are distributed in areas where high numbers of sebaceous glands are found, most commonly the chest, arms, axillae and neck. Several reports of localized SM limited to the scalp, face, retro-auricular region, groin and nasal region have been reported [1-3]. Herein, we report a case of SM localized to the scrotum. The appearance of multiple cystic lesions involving the scrotum, especially in unmarried men, is highly embarrassing.

Case Report

A 22-year old unmarried male presented with multiple cystic firm lesions over scrotum. These lesions had gradually grown larger and increased in number over a period of three years. On physical examination, asymptomatic multiple smooth yellow and skincolored cystic nodules were palpable on the whole scrotum, there were no central punctum; however, no lesions were detected in other locations, including the trunk, extremities, and face. The diameters of the lesions ranged from 1cm to 3 cms (Figure 1,2). There were no signs of inflammation in any of the lesions. The patient’s past and family histories were non-contributory. The results of laboratory blood tests did not show any evidence of infection or inflammation. Patient underwent excision of lesions en-mass (Figure 3) under spinal anaesthesia and primary closure was done (Figure 4) and specimen sent for histopathology. Subsequent histopathological examination revealed cysts within the lower dermis and subcutaneous fat. The folded cystic wall was lined with stratified squamous epithelium and contained flattened sebaceous gland cells (Figure 5).